Cryoglobulinemia natural history, complications and prognosis
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Feham Tariq, MD [2]
Overview
Natural History
Complications
The complications of cryoglobulinemia are as follows:
- Rapidly progressive neuropathy
- Heart failure
- Digital ischemia threatening amputation
- Diffuse alveolar hemorrhage resulting in hemoptysis
- Respiratory failure
- Stroke
- End stage renal disease
Prognosis
Patients having severe manifestations of the disease such as pulmonary vasculitis, end-stage renal disease, cardiac vasculitis and central nervous system vasculitis have generally poor prognosis of the disease. The prognosis of cryoglobulinemia depends on the organ system involved and varies accordingly.
| Organ system involved | Survival rate |
|---|---|
| Glomerulonephritis | 79% |
| Pulmonary vasculitis | 22% |
| Central nervous system vasculitis | 66% |
| Gastrointestinal vasculitis | 67% |
| Cardiac vasculitis | 100% |