Idiopathic interstitial pneumonia differential diagnosis

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Ahmed Zaghw, M.D. [2]


Differential diagnosis

Hypersensitivity pneumonia is always confusing a hypersensitivity pneumonitis especially if the triggering factor or the environmental exposure can be identified.

Extensive serological evaluation is needed to rule out collagen diseases [1]. Clinical, serologic, HRCT, and histolpathological findings may be helpful in distinguishing IIPs from ILD associated with collagen vascular disease CVDs. [2] [3] [4] [5]. However a significant number of patients have overlapping serological findings, yet they do not meet the fully defined criteria for CVDs and still are categorized as IIPs.

References

  1. Raghu, G.; Collard, HR.; Egan, JJ.; Martinez, FJ.; Behr, J.; Brown, KK.; Colby, TV.; Cordier, JF.; Flaherty, KR. (2011). "An official ATS/ERS/JRS/ALAT statement: idiopathic pulmonary fibrosis: evidence-based guidelines for diagnosis and management". Am J Respir Crit Care Med. 183 (6): 788–824. doi:10.1164/rccm.2009-040GL. PMID 21471066. Unknown parameter |month= ignored (help)
  2. Felício, CH.; Parra, ER.; Capelozzi, VL. "Idiopathic and collagen vascular disease nonspecific interstitial pneumonia: clinical significance of remodeling process". Lung. 185 (1): 39–46. doi:10.1007/s00408-006-0104-2. PMID 17294340.
  3. Park, JH.; Kim, DS.; Park, IN.; Jang, SJ.; Kitaichi, M.; Nicholson, AG.; Colby, TV. (2007). "Prognosis of fibrotic interstitial pneumonia: idiopathic versus collagen vascular disease-related subtypes". Am J Respir Crit Care Med. 175 (7): 705–11. doi:10.1164/rccm.200607-912OC. PMID 17218621. Unknown parameter |month= ignored (help)
  4. Hwang, JH.; Misumi, S.; Sahin, H.; Brown, KK.; Newell, JD.; Lynch, DA. "Computed tomographic features of idiopathic fibrosing interstitial pneumonia: comparison with pulmonary fibrosis related to collagen vascular disease". J Comput Assist Tomogr. 33 (3): 410–5. doi:10.1097/RCT.0b013e318181d551. PMID 19478636.
  5. Song, JW.; Do, KH.; Kim, MY.; Jang, SJ.; Colby, TV.; Kim, DS. (2009). "Pathologic and radiologic differences between idiopathic and collagen vascular disease-related usual interstitial pneumonia". Chest. 136 (1): 23–30. doi:10.1378/chest.08-2572. PMID 19255290. Unknown parameter |month= ignored (help)

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