Hemophilia CT

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Simrat Sarai, M.D. [2]

Overview

On CT, Hemophilia is characterized by haemorrhage into joints or soft-tissue.

CT

The hallmark of the disease is haemorrhage, particularly into joints and/or soft-tissue, with three main radiological consequences:

  • haemophilic arthropathy occurring in almost all individuals
  • haemophilic pseudotumour occurring in ~2%
  • soft tissue haematoma formation, may lead to contractures 3
  • serious life-threatening haemorrhage (intracranial, thoracic, abdominal)[1]

(Images courtesy of RadsWiki)

References

  1. "Hemophilia Radiographic features".

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