Autoimmune polyendocrine syndrome classification: Difference between revisions

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Revision as of 19:07, 3 October 2017

Autoimmune polyendocrine syndrome Microchapters

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief:

Overview

  • Autoimmune polyendocrine syndrome can be categorized into three different types namely type 1 {also called autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED)}, type 2 and IPEX syndrome.

There is no established system for the classification of [disease name].

OR

[Disease name] may be classified according to [classification method] into [number] subtypes/groups: [group1], [group2], [group3], and [group4].

OR

[Disease name] may be classified into [large number > 6] subtypes based on [classification method 1], [classification method 2], and [classification method 3]. [Disease name] may be classified into several subtypes based on [classification method 1], [classification method 2], and [classification method 3].



Classification

Type 1

Template:Seealso Autoimmune polyendocrine syndrome, type 1 is also known as the candidiasis-hypoparathyroidism-Addison's disease-syndrome after its main features:

A EU-funded consortium is currently doing translational research on this condition and has establised w webpage at EurAPS.


 
 
 
 
 
 
 
 
Autoimmune polyendocrine syndrome (APS)
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
APS type 1
 
 
 
 
APS type 2
 
 
 
 
APS type 3
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
D01
 
 
 
 
D02
 
 
 
 
D03




Type 2

Autoimmune polyendocrine syndrome, type 2 also known as "Schmidt's syndrome". Features of this syndrome are:

  • Addison's disease
  • hypothyroidism
  • diabetes mellitus (type 1)
  • less common associations:
    • hypogonadism
    • vitiligo

Some researchers favour splitting this syndrome into three distinct syndromes (numbering 2, 3 and 4), but research evidence for these distinct combinations is not convincing.

XPID

The most serious but rarest form is the X-linked polyendocrinopathy, immunodeficiency and diarrhea-syndrome, also called IPEX. Most patients develop diabetes and diarrhea as neonates and many die due to autoimmune activity against many organs. Boys are affected, while girls are carriers and might suffer mild disease.

Other diseases

Other diseases featuring polyendocrine autoimmunity:

Classification

  • There is no established system for the classification of [disease name].

OR

  • [Disease name] may be classified according to [classification method] into [number] subtypes/groups:
    • [group1]
    • [group2]
    • [group3]
    • [group4]

OR

  • [Disease name] may be classified into [large number > 6] subtypes based on:
    • [classification method 1]
    • [classification method 2]
    • [classification method 3]
  • [Disease name] may be classified into several subtypes based on:
    • [classification method 1]
    • [classification method 2]
    • [classification method 3]

OR

  • Based on the duration of symptoms, [disease name] may be classified as either acute or chronic.

OR

  • If the staging system involves specific and characteristic findings and features:
  • According to the [staging system + reference], there are [number] stages of [malignancy name] based on the [finding1], [finding2], and [finding3]. Each stage is assigned a [letter/number1] and a [letter/number2] that designate the [feature1] and [feature2].

OR

  • The staging of [malignancy name] is based on the [staging system].

OR

  • There is no established system for the staging of [malignancy name].

References

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