Tricuspid atresia: Difference between revisions

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{{Infobox_Disease |
{{Infobox_Disease |
   Name          = Tricuspid atresia |
   Name          = {{PAGENAME}} |
  Image          = Diagram of the human heart (cropped).svg |
  Caption        = Anterior (frontal) view of the opened heart. White arrows indicate normal blood flow. (Tricuspid valve labeled at bottom left.) |
   DiseasesDB    = |
   DiseasesDB    = |
   ICD10          = {{ICD10|Q|22|4|q|20}} |
   ICD10          = {{ICD10|Q|22|4|q|20}} |
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   MeshID        = D018785 |
   MeshID        = D018785 |
}}
}}
{{Search infobox}}
{{WikiDoc Cardiology Network Infobox}}
{{CMG}}
{{CMG}}


'''Associate Editor-in-Chief:''' [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]
'''Associate Editor-in-Chief:''' [[User:KeriShafer|Keri Shafer, M.D.]] [mailto:kshafer@bidmc.harvard.edu]


{{Editor Join}}
==[[Tricuspid atresia overview|Overview]]==


==Overview==
==[[Tricuspid atresia pathophysiology|Pathophysiology]]==
'''Tricuspid atresia''' is a form of [[congenital heart disease]] whereby there is a complete absence of the [[tricuspid valve]]. Therefore, there is an absence of right atrioventricular connection. This leads to a [[hypoplastic]] or an absence of the [[right ventricle]].


==Pathophysiology==
==Diagnosis==
This defect occurs during prenatal development.  Because of the lack of an A-V connection, an [[atrial septal defect]] (ASD) ''must'' be present to maintain blood flow. Also, since there is a lack of a right ventricle there ''must'' be a way to pump blood into the [[pulmonary arteries]], and this is accomplished by a [[ventricular septal defect]] (VSD).
[[Tricuspid atresia history and symptoms|History and symptoms]]
 
Blood is mixed in the [[left atrium]]. Because the only way the pulmonary circulation receives blood is through the VSD, a [[patent ductus arteriosus]] is usually also formed to increase pulmonary flow.
 
==Clinical manifestations==
* progressive [[cyanosis]]
* [[Poor feeding]]
* [[Tachypnea]] over the first 2 weeks of life
* Holosystolic [[heart murmur|murmur]] due to the VSD
* Superior axis deviation and [[left ventricular hypertrophy]] (since it must pump blood to both the pulmonary and systemic systems)
* ''normal'' heart size


==Treatment==
==Treatment==
* [[PGE1]] to maintain [[patent ductus arteriosus]]
[[Tricuspid atresia surgery|Surgery]]
* Modified [[Blalock-Taussig]] shunt to maintain pulmonary blood flow by placing a Gortex conduit between the [[subclavian artery]] and the [[pulmonary artery]].
* Cavopulmonary anastomosis (hemi-Fontan or bidirectional Glenn) to provide stable pulmonary flow
* [[Fontan procedure]] to redirect [[inferior vena cava]] and [[hepatic vein]] flow into the pulmonary circulation


==External Links==
==External Links==
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* Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843
* Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843


[[Category:Cardiovascular system]]
[[Category:Cardiology]]
[[Category:Congenital heart disease]]
[[Category:Pediatrics]]


{{Congenital malformations and deformations of circulatory system}}
{{WH}}
{{Electrocardiography}}
{{WS}}
{{Circulatory system pathology}}
{{SIB}}
 
[[category:cardiovascular system]]
[[category:Cardiology]]
[[category:Congenital heart disease]]
[[category:Pediatrics]]
 
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Revision as of 19:48, 13 July 2011

Tricuspid atresia
ICD-10 Q22.4
ICD-9 746.1
OMIM 605067
MedlinePlus 001110
eMedicine med/2313 
MeSH D018785

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Associate Editor-in-Chief: Keri Shafer, M.D. [2]

Overview

Pathophysiology

Diagnosis

History and symptoms

Treatment

Surgery

External Links

Additional Reading

  • Moss and Adams' Heart Disease in Infants, Children, and Adolescents Hugh D. Allen, Arthur J. Moss, David J. Driscoll, Forrest H. Adams, Timothy F. Feltes, Robert E. Shaddy, 2007 ISBN 0781786843

Template:WH Template:WS

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