Right ventricular outflow tract obstruction pulmonary subvalvular stenosis
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]
Associate Editor-in-Chief: Keri Shafer, M.D. [3]
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Anatomy
- There is hypertrophy of the infundibular muscle causing obstruction.
- The isolated form is rare, more commonly develops in response to an underlying VSD.
Clinical Features
- Similar to valvar pulmonic stenosis.
- No ejection click in contrast to valvar pulmonic stenosis.
- No poststenotic dilation of the pulmonary artery in contrast to valvar pulmonic stenosis.