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'''For patient information page click [[{{PAGENAME}} (patient information)|here]]'''
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{{Retroperitoneal fibrosis}}
{{SCC}}
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{{Editor Join}}
{{SK}} Ormond's disease; fibrosis, inflammatory perianeurysmal; fibrosis, perianeurysmal inflammatory; inflammatory fibrosis, perianeurysmal; inflammatory perianeurysmal fibrosis; Ormond disease; perianuerysmal fibrosis, inflammatory; perianeurysmal inflammatory fibrosis; periaortitis, chronic


==Overview==
==[[Retroperitoneal fibrosis overview|Overview]]==


'''Retroperitoneal fibrosis''' or '''Ormond's disease''' is a disease featuring the proliferation of fibrous tissue in the [[retroperitoneum]], the compartment of the body containing the [[kidney]]s, [[aorta]], [[renal tract]] and various other structures. It may present with [[lower back pain]], [[renal failure]], [[hypertension]], [[deep vein thrombosis]] and other obstructive symptoms.
==[[Retroperitoneal fibrosis pathophysiology|Pathophysiology]]==


==Causes==
==[[Retroperitoneal fibrosis causes|Causes]]==
Its association with various immune-related conditions and response to [[immunosuppression]] have led to speculations as to the [[autoimmune disorder|autoimmune]] etiology of idiopathic RPF. One-third of the cases are secondary to [[malignancy]], medication ([[methysergide]], [[hydralazine]], [[beta blocker]]s), [[aortic aneurysm]] or certain infections.
 
==[[Retroperitoneal fibrosis differential diagnosis|Differentiating Retroperitoneal fibrosis from other Diseases]]==
 
==[[Retroperitoneal fibrosis epidemiology and demographics|Epidemiology and Demographics]]==
 
==[[Retroperitoneal fibrosis natural history, complications and prognosis|Natural History, Complications and Prognosis]]==
 
==Diagnosis==
[[Retroperitoneal fibrosis history and symptoms|History and Symptoms]] | [[Retroperitoneal fibrosis physical examination|Physical Examination]] | [[Retroperitoneal fibrosis laboratory findings|Laboratory Findings]] | [[Retroperitoneal fibrosis CT|CT]] | [[Retroperitoneal fibrosis MRI|MRI]] | [[Retroperitoneal fibrosis other imaging findings|Other Imaging Findings]] | [[Retroperitoneal fibrosis other diagnostic studies|Other Diagnostic Studies]]


==Treatment==
==Treatment==
In the absence of severe urinary tract obstruction (which generally requires [[surgery]] with omental wrapping) treatment is generally with [[glucocorticoid]]s initially, followed by [[DMARD]]s either as steroid-sparing agents or if refractory on steroids. The SERM [[tamoxifen]] has shown to improve the condition in various small trials, although the exact mechanism of its action remains unclear.
[[Retroperitoneal fibrosis medical therapy|Medical Therapy]] | [[Retroperitoneal fibrosis surgery|Surgery]] | [[Retroperitoneal fibrosis primary prevention|Primary Prevention]] | [[Retroperitoneal fibrosis cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Retroperitoneal fibrosis future or investigational therapies|Future or Investigational Therapies]]


==References==
==Case Studies==
:[[Retroperitoneal fibrosis case study one|Case #1]]
 
==External links==
* van Bommel EF. Retroperitoneal fibrosis. ''Neth J Med'' 2002;60:231-42. PMID 12365466.
* van Bommel EF. Retroperitoneal fibrosis. ''Neth J Med'' 2002;60:231-42. PMID 12365466.
* Ormond JK. Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process. ''J Urol'' 1948;59:1072-79.
* Ormond JK. Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process. ''J Urol'' 1948;59:1072-79.
* Ormond JK. Idiopathic retroperitoneal fibrosis: a discussion of the etiology. ''J Urol'' 1965;94:385-90.
* Ormond JK. Idiopathic retroperitoneal fibrosis: a discussion of the etiology. ''J Urol'' 1965;94:385-90.


==External links==
* {{WhoNamedIt|synd|1712}}
{{SIB}}


[[Category:Urology]]
[[Category:Urology]]

Latest revision as of 15:59, 8 November 2012

For patient information page click here

Retroperitoneal fibrosis
ICD-10 N13.5
ICD-9 593.4
DiseasesDB 11445
MeSH D012185

Retroperitoneal fibrosis Microchapters

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Overview

Pathophysiology

Causes

Differentiating Retroperitoneal fibrosis from other Diseases

Epidemiology and Demographics

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms

Physical Examination

Laboratory Findings

CT

MRI

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Primary Prevention

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

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Steven C. Campbell, M.D., Ph.D.

Synonyms and keywords: Ormond's disease; fibrosis, inflammatory perianeurysmal; fibrosis, perianeurysmal inflammatory; inflammatory fibrosis, perianeurysmal; inflammatory perianeurysmal fibrosis; Ormond disease; perianuerysmal fibrosis, inflammatory; perianeurysmal inflammatory fibrosis; periaortitis, chronic

Overview

Pathophysiology

Causes

Differentiating Retroperitoneal fibrosis from other Diseases

Epidemiology and Demographics

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms | Physical Examination | Laboratory Findings | CT | MRI | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical Therapy | Surgery | Primary Prevention | Cost-Effectiveness of Therapy | Future or Investigational Therapies

Case Studies

Case #1

External links

  • van Bommel EF. Retroperitoneal fibrosis. Neth J Med 2002;60:231-42. PMID 12365466.
  • Ormond JK. Bilateral ureteral obstruction due to envelopment and compression by an inflammatory retroperitoneal process. J Urol 1948;59:1072-79.
  • Ormond JK. Idiopathic retroperitoneal fibrosis: a discussion of the etiology. J Urol 1965;94:385-90.

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