Hypertrophic cardiomyopathy resident survival guide: Difference between revisions

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{{familytree | | | | | | | | A01 |A01=<b>Left Ventricular Hypertrophy</b>}}  
{{familytree | | | | | | | | A01 |A01=<b>Left Ventricular Hypertrophy</b>}}  
{{familytree | | | | |,|-|-|-|+|-|-|-|-|.| | | }}
{{familytree | | | | |,|-|-|-|+|-|-|-|-|.| | | }}
{{familytree | | | B01 | | | B02 | | | B03 | | |B01=B01|B02=B02|B03=}}
{{familytree | | | B01 | | | B02 | | | B03 | | |B01=<b>Sarcomere Mutation</b>|B02=<b>Without Extracardiac or Metabolic Findings + Genetic Substrate Unresolved</b>|B03=<b>With Extracardiac or Metabolic Findings Associated With or Without Mutant Gene</b>}}
{{familytree | | | |`|-|-|v|-|'| | | | |!| }}
{{familytree | | | |`|-|-|v|-|'| | | | |!| }}
{{familytree | | | | | | C01 | | | | | C03 | | |C01=|C02=
{{familytree | | | | | | C01 | | | | | C03 | | |C01=<b>Hypertrophic Cardiomyopathy</b>|C02=<b>Syndrome with Left Ventricular Hypertrophy</b>}}
{{familytree/end}}
{{familytree/end}}
==Causes==
==Causes==

Revision as of 15:42, 6 March 2015

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief:

Hypertrophic cardiomyopathy resident survival guide Microchapters
Overview
Classification
Causes
FIRE
Diagnosis
Treatment
Do's
Dont's

Overview

Hypertrophic Cardiomyopathy is defined by LV hypertrophy associated with nondilated ventricular chambers. HCM is usually recognized by maximal LV wall thickness ≥15 mm. Wall thickness of 13 to 14 mm is considered borderline if there are other compelling information (eg, family history of HCM), based on echocardiography. The diagnostic imaging mainly focused on echocardiography, however cardiovascular magnetic resonance (CMR) is used with increasing frequency.[1]

Classification

 
 
 
 
 
 
 
Left Ventricular Hypertrophy
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Sarcomere Mutation
 
 
Without Extracardiac or Metabolic Findings + Genetic Substrate Unresolved
 
 
With Extracardiac or Metabolic Findings Associated With or Without Mutant Gene
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
Hypertrophic Cardiomyopathy
 
 
 
 
{{{ C03 }}}
 
 

Causes

Life Threatening Causes

Common Causes

FIRE: Focused Initial Rapid Evaluation

A Focused Initial Rapid Evaluation (FIRE) should be performed to identify patients in need of immediate intervention.

 
 
 
 
 
 
 
A01
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
B01
 
 
 
 
 
 
 
B02
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
C01
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
D01
 
D02
 
 
 
 
 
D03
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
E01
 
 
 
 
 
 
E02
 
 
E03
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
F01
 
 
F02

Complete Diagnostic Approach

 
 
 
 
 
 
 
A01
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
B01
 
 
 
 
 
 
 
B02
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
C01
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
D01
 
D02
 
 
 
 
 
D03
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
E01
 
 
 
 
 
 
E02
 
 
E03
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
F01
 
 
F02

Treatment

shown

hidden

Do's

Dont's

References

  1. American College of Cardiology Foundation/American Heart Association Task Force on Practice. American Association for Thoracic Surgery. American Society of Echocardiography. American Society of Nuclear Cardiology. Heart Failure Society of America. Heart Rhythm Society; et al. (2011). "2011 ACCF/AHA guideline for the diagnosis and treatment of hypertrophic cardiomyopathy: a report of the American College of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines". J Thorac Cardiovasc Surg. 142 (6): e153–203. doi:10.1016/j.jtcvs.2011.10.020. PMID 22093723.