Angiomyolipoma epidemiology and demographics
|
Angiomyolipoma Microchapters |
|
Diagnosis |
|---|
|
Treatment |
|
Case Studies |
|
Angiomyolipoma epidemiology and demographics On the Web |
|
American Roentgen Ray Society Images of Angiomyolipoma epidemiology and demographics |
|
Risk calculators and risk factors for Angiomyolipoma epidemiology and demographics |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2], Faizan Sheraz, M.D. [3] Angiomyolipomas are the most common benign solid renal lesion and also the most fat containing lesion of the kidneys. The majority of angiomyolipomas are sporadic (80%) and are typically identified in adults (mean age of presentation 43 years), with a strong female predilection (F:M of 4:1) 7,9. The remaining 20% are seen in association with phakomatoses, the vast majority in the setting of tuberous sclerosis, although they have also been described in setting of Von Hippel-Lindau syndrome (VHL) and neurofibromatosis type 1 (NF1) 5,7. In these cases they present earlier (usually identified by the age of 10 years), are larger, and are far more numerous. They are more likely to be fat-poor which accounts for their earlier presentation 2,6-7.
Incidence
The incidence is about 0.3-3%. It occurs in more than 50% of individuals with tuberous sclerosis, often bilaterally.
Gender
Angiomyolipoma is twice as common in females as in males.