Cardiac disease in pregnancy and marfan's syndrome: Difference between revisions

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*Autosomal dominant inheritance pattern (counseling is essential)
*Autosomal dominant inheritance pattern (counseling is essential)
*Major risk is [[aortic dissection]]     
*Major risk is [[aortic dissection]]     
::* Most common in 3rd trimester or 1st stage of labor
* Most common in 3rd trimester or 1st stage of labor
::* Increases with enlarging aortic root diameter
* Increases with enlarging aortic root diameter
::* Surgery recommended pre-conception if root diameter >40 mm
 
* Prophylactic [[beta-blockers]] appear to be helpful
*Close follow-up with serial echocardiography
 
*'''Surgery:'''
::*Surgery recommended pre-conception if root diameter >40 mm
::* Surgery recommend during gestation if > 55 mm
::* Surgery recommend during gestation if > 55 mm
::* Prophylactic [[beta-blockers]] appear to be helpful
*Close follow-up with serial echocardiography


==References==
==References==

Revision as of 04:23, 17 April 2012

Cardiac disease in pregnancy Microchapters

Home

Overview

Pathophysiology

Epidemiology and Demographics

Risk Factors

Diagnosis

History and Symptoms

Physical Examination

Electrocardiogram

Exercise Testing

Radiation Exposure

Chest X Ray

Echocardiography

MRI

CT

Catheterization:

Pulmonary artery catheterization
Cardiac catheterization
Cardiac Ablation

Treatment

Cardiovascular Drugs in Pregnancy

Labor and delivery

Resuscitation in Late Pregnancy

Contraindications to pregnancy

Special Scenarios:

I. Pre-existing Cardiac Disease:
Congenital Heart Disease
Repaired Congenital Heart Disease
Pulmonary Hypertension
Rheumatic Heart Disease
Connective Tissue Disorders
II. Valvular Heart Disease:
Mitral Stenosis
Mitral Regurgitation
Aortic Insufficiency
Aortic Stenosis
Mechanical Prosthetic Valves
Tissue Prosthetic Valves
III. Cardiomyopathy:
Dilated Cardiomyopathy
Hypertrophic Cardiomyopathy
Peripartum Cardiomyopathy
IV. Cardiac diseases that may develop During Pregnancy:
Arrhythmias
Acute Myocardial Infarction
Hypertension

Cardiac disease in pregnancy and marfan's syndrome On the Web

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Blogs on Cardiac disease in pregnancy and marfan's syndrome

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Risk calculators and risk factors for Cardiac disease in pregnancy and marfan's syndrome

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]

Overview

  • Autosomal dominant inheritance pattern (counseling is essential)
  • Major risk is aortic dissection
  • Most common in 3rd trimester or 1st stage of labor
  • Increases with enlarging aortic root diameter
  • Prophylactic beta-blockers appear to be helpful
  • Close follow-up with serial echocardiography
  • Surgery:
  • Surgery recommended pre-conception if root diameter >40 mm
  • Surgery recommend during gestation if > 55 mm

References


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