Vasculitis resident survival guide: Difference between revisions

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==Causes==
==Causes==
===Life Threatening Causes===
{| class="wikitable"
Life-threatening causes include conditions that may result in death or permanent disability within 24 hours if left untreated.
|+ The 2012 Chapel Hill Consensus Conference (CHCC) classified the vasculitides as follows:
* [[Life threatening cause 1]]
|-
* [[Life threatening cause 2]]
! Large Vessel Vasculitis
* [[Life threatening cause 3]]
|-
| Takayasu arteritis
|-
| Giant cell arteritis
|-
! Medium vessel vasculitis
|-
| Polyarteritis nodosa
|-
| Kawasaki disease
|-
! Small vessel vasculitis
|-
| ANCA-associated vasculitis: Microscopic polyangiitis, Granulomatosis with polyangiitis (Wegener's), and Eosinophilic granulomatosis with polyangiitis (Churg-Strauss).
|-
| Immune complex small-vessel vasculitis: Anti-glomerular basement membrane disease, Cryoglobulinemic vasculitis, IgA vasculitis (Henoch-Schönlein), and Hypocomplementemic urticarial vasculitis (anti-C1q vasculitis)
|-
! Variable-vessel vasculitis
|-
| Behçet's syndrome
|-
| Cogan's syndrome
|-
! Single-organ vasculitis
|-
| Cutaneous leukocytoclastic angiitis
|-
| Cutaneous arteritis
|-
| Primary central nervous system vasculitis
|-
| Isolated aortitis
|-
! Vasculitis associated with systemic disease
|-
| Lupus vasculitis
|-
| Rheumatoid vasculitis
|-
| Sarcoid vasculitis
|-
| Others
|-
! Vasculitis associated with probable etiology
|-
| Hepatitis C virus-associated cryoglobulinemic vasculitis
|-
| Hepatitis B virus-associated vasculitis
|-
| Syphilis-associated aortitis
|-
| Drug-associated immune complex vasculitis
|-
| Drug-associated ANCA-associated vasculitis
|-
| Cancer-associated vasculitis
|-
| other


===Common Causes===
|}
* [[Common cause 1]]
* [[Common cause 2]]
* [[Common cause 3]]
* [[Common cause 4]]
* [[Common cause 5]]


==Diagnosis==
==Diagnosis==

Revision as of 18:29, 19 May 2021


Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Dina Elantably, MD, MSc[2]


Synonyms and keywords: Arteritis, Angiitis, Vasculitides (plural)

Overview

Vasculitis is the presence of inflammatory leukocytes in the walls of the blood vessels with reactive damage to mural structures leading to compromise of the lumen with downstream ischemia, necrosis, and bleeding. The exact pathogenesis is unknown, and vasculitis can be primary or secondary to underlying disease. The extent and severity of vasculitides may vary from self-limited cutaneous vasculitis to severe fatal systemic vasculitides.

Causes

The 2012 Chapel Hill Consensus Conference (CHCC) classified the vasculitides as follows:
Large Vessel Vasculitis
Takayasu arteritis
Giant cell arteritis
Medium vessel vasculitis
Polyarteritis nodosa
Kawasaki disease
Small vessel vasculitis
ANCA-associated vasculitis: Microscopic polyangiitis, Granulomatosis with polyangiitis (Wegener's), and Eosinophilic granulomatosis with polyangiitis (Churg-Strauss).
Immune complex small-vessel vasculitis: Anti-glomerular basement membrane disease, Cryoglobulinemic vasculitis, IgA vasculitis (Henoch-Schönlein), and Hypocomplementemic urticarial vasculitis (anti-C1q vasculitis)
Variable-vessel vasculitis
Behçet's syndrome
Cogan's syndrome
Single-organ vasculitis
Cutaneous leukocytoclastic angiitis
Cutaneous arteritis
Primary central nervous system vasculitis
Isolated aortitis
Vasculitis associated with systemic disease
Lupus vasculitis
Rheumatoid vasculitis
Sarcoid vasculitis
Others
Vasculitis associated with probable etiology
Hepatitis C virus-associated cryoglobulinemic vasculitis
Hepatitis B virus-associated vasculitis
Syphilis-associated aortitis
Drug-associated immune complex vasculitis
Drug-associated ANCA-associated vasculitis
Cancer-associated vasculitis
other

Diagnosis

Shown below is an algorithm summarizing the diagnosis of [[disease name]] according the the [...] guidelines.

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 

Treatment

Shown below is an algorithm summarizing the treatment of [[disease name]] according the the [...] guidelines.

 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 
 

Do's

  • The content in this section is in bullet points.

Don'ts

  • The content in this section is in bullet points.

References


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