Bile duct cyst: Difference between revisions

Jump to navigation Jump to search
Line 67: Line 67:
==Presentation==
==Presentation==


Most of them present in 1st year of life; adult presentation is rare and usually at this stage is associated with complication . Classic triad of '''intermittent abdominal pain, [[jaundice]], and a [[right upper quadrant]] [[abdominal mass]]''' is found only in minority of patients.
Most of them present in 1st year of life; adult presentation is rare and usually at this stage is associated with complication . Classic triad of [[abdominal pain|intermittent abdominal pain]], [[jaundice]], and a [[right upper quadrant]] [[abdominal mass]] is found only in minority of patients.


==References==
==References==

Revision as of 01:06, 8 April 2009

Bile duct cyst
MRCP: Type 4 bile duct cyst.
Image courtesy of RadsWiki

WikiDoc Resources for Bile duct cyst

Articles

Most recent articles on Bile duct cyst

Most cited articles on Bile duct cyst

Review articles on Bile duct cyst

Articles on Bile duct cyst in N Eng J Med, Lancet, BMJ

Media

Powerpoint slides on Bile duct cyst

Images of Bile duct cyst

Photos of Bile duct cyst

Podcasts & MP3s on Bile duct cyst

Videos on Bile duct cyst

Evidence Based Medicine

Cochrane Collaboration on Bile duct cyst

Bandolier on Bile duct cyst

TRIP on Bile duct cyst

Clinical Trials

Ongoing Trials on Bile duct cyst at Clinical Trials.gov

Trial results on Bile duct cyst

Clinical Trials on Bile duct cyst at Google

Guidelines / Policies / Govt

US National Guidelines Clearinghouse on Bile duct cyst

NICE Guidance on Bile duct cyst

NHS PRODIGY Guidance

FDA on Bile duct cyst

CDC on Bile duct cyst

Books

Books on Bile duct cyst

News

Bile duct cyst in the news

Be alerted to news on Bile duct cyst

News trends on Bile duct cyst

Commentary

Blogs on Bile duct cyst

Definitions

Definitions of Bile duct cyst

Patient Resources / Community

Patient resources on Bile duct cyst

Discussion groups on Bile duct cyst

Patient Handouts on Bile duct cyst

Directions to Hospitals Treating Bile duct cyst

Risk calculators and risk factors for Bile duct cyst

Healthcare Provider Resources

Symptoms of Bile duct cyst

Causes & Risk Factors for Bile duct cyst

Diagnostic studies for Bile duct cyst

Treatment of Bile duct cyst

Continuing Medical Education (CME)

CME Programs on Bile duct cyst

International

Bile duct cyst en Espanol

Bile duct cyst en Francais

Business

Bile duct cyst in the Marketplace

Patents on Bile duct cyst

Experimental / Informatics

List of terms related to Bile duct cyst

Please Take Over This Page and Apply to be Editor-In-Chief for this topic: There can be one or more than one Editor-In-Chief. You may also apply to be an Associate Editor-In-Chief of one of the subtopics below. Please mail us [1] to indicate your interest in serving either as an Editor-In-Chief of the entire topic or as an Associate Editor-In-Chief for a subtopic. Please be sure to attach your CV and or biographical sketch.

Overview

Bile duct cysts are congenital conditions associated with benign cystic dilatation of bile ducts. They are uncommon in western countries[1] [2] but not as rare in East Asian nations like Japan and China.

Classification

According to the Todani system, there are five types of bile duct cysts.[3].

Type 1: Choledochal Cyst

  • Account for 80% to 90% of all bile duct cysts
  • Characterized by fusiform dilation of the extrahepatic bile duct
  • Theorized that choledochal cysts form as the result of reflux of pancreatic secretions into the bile duct via anomalous pancreaticobiliary junction.
  • Cyst should be resected completely to prevent associated complications (i.e. ascending cholangitis and malignant transformation).

Type 2: Diverticulum

  • Accounts for 3% of all bile duct cysts
  • Represents a true diverticulum.
  • Saccular outpouchings arising from the supraduodenal extrahepatic bile duct or the intrahepatic bile ducts.

Type 3: Choledochocele

  • Accounts for 5% of all bile duct cysts
  • Represents protrusion of a focally dilated, intramural segment of the distal common bile duct into the duodenum.
  • Choledochoceles may be successfully managed with endoscopic sphincterotomy, surgical excision, or both, in symptomatic patients.

Type 4: Multiple Communicating Intra and Extrahepatic Duct Cysts

  • Second most common type of bile duct cysts (10%)
  • Subdivided into subtypes A and B.
    • Type 4A: Fusiform dilation of the entire extrahepatic bile duct with extension of dilation of the intrahepatic bile ducts
    • Type 4B: Multiple cystic dilations involving only the extrahepatic bile duct.

Images courtesy of RadsWiki

Type 5: Caroli's Disease

  • Caroli's disease is a rare form of congenital biliary cystic disease manifested by cystic dilations of intrahepatic bile ducts
  • Association with benign renal tubular ectasia and other forms of renal cystic disease.

Presentation

Most of them present in 1st year of life; adult presentation is rare and usually at this stage is associated with complication . Classic triad of intermittent abdominal pain, jaundice, and a right upper quadrant abdominal mass is found only in minority of patients.

References

  1. Liu YB, Wang JW, Devkota KR; et al. (2007). "Congenital choledochal cysts in adults: twenty-five-year experience". Chin. Med. J. 120 (16): 1404–7. PMID 17825168.
  2. Yu, Jinxing, Turner, Mary Ann, Fulcher, Ann S., Halvorsen, Robert A. Congenital Anomalies and Normal Variants of the Pancreaticobiliary Tract and the Pancreas in Adults: Part 1, Biliary Tract. Am. J. Roentgenol. 2006 187: 1536-1543
  3. Todani T, Watanabe Y, Narusue M, Tabuchi K, Okajima K (1977). "Congenital bile duct cysts: Classification, operative procedures, and review of thirty-seven cases including cancer arising from choledochal cyst". Am. J. Surg. 134 (2): 263–9. PMID 889044.

Template:Gastroenterology Template:SIB


Template:WikiDoc Sources