Rhabdomyoma surgery
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Rhabdomyoma Microchapters |
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Rhabdomyoma surgery On the Web |
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American Roentgen Ray Society Images of Rhabdomyoma surgery |
Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Nima Nasiri, M.D.[2]
Overview
Rhabdomyoma is a benign tumor of striated muscle. Rhabdomyomas are rare and can be classified into cardiac type and extracardiac type.The most common primary benign pediatric tumor of the heart is cardiac rhabdomyoma which can be seen mainly in fetal life and children, second most common primary benign cardiac tumor in children is fibroma. Most tumors regress spontaneously, prognosis depends on the location of tumor and size. Cardiac rhabdomyoma is strongly associated with tuberous sclerosis.
Surgery
Adult rhabdomyoma
- Surgical resection of the tumor can only be performed for patients with adult rhabdomyoma if airway obstruction is diagnosed, there have been reports of rare cases of laryngeal rhabdomyoma which may cause breathing difficulty for patients.[1]
Cardiac rhabdomyoma
- In patients with cardiac rhabdomyoma who have symptoms of severe outflow tract obstruction or arrhythmias, surgical intervention can be helpful. Surgical management involves removal of the part of the tumor causing obstruction without complete excision of the entire lesion.[2]
References
- ↑ Pinho MM, de Carvalho E Castro J, Ramos RG (October 2013). "Adult rhabdomyoma of the larynx". Int Arch Otorhinolaryngol. 17 (4): 415–8. doi:10.1055/s-0033-1351671. PMC 4399195. PMID 25992049. Vancouver style error: missing comma (help)
- ↑ Norawat R, Sarkar D, Maybauer MO (2018). "Perioperative management of critical right ventricular inflow obstruction from right atrial rhabdomyoma". Ann Card Anaesth. 21 (4): 430–432. doi:10.4103/aca.ACA_233_17. PMC 6206783. PMID 30333341.