Lipoid congenital adrenal hyperplasia epidemiology and demographics
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Lipoid congenital adrenal hyperplasia Microchapters |
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
Overview
Epidemiology and Demographics
Lipoid CAH is quite rare in European and North American populations. Most cases have occurred in Japan and Korea (where the incidence is 1 in 300,000 births) and Palestinian Arabs. Despite autosomal recessive inheritance, there has been an unexplained preponderance of genetic females in reported cases