Cornea verticillata

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

Cornea verticillata: A bilateral, whorl-like corneal pattern of cream colored lines in a patient with Fabry disease.

Cornea verticillata, also called Fleischer vortex,[1] Vortex keratopathy or Whorl keratopathy, is a condition characterised by corneal deposits at the level of the basal epithelium forming a faint golden-brown whorl pattern. It is seen in Fabry disease or in case of prolonged amiodarone intake.[2]

Presentation

No ocular complaints or visual difficulty is usually present.[2][3]

Pathophysiology

This keratopathy is probably a type of drug-induced lipidosis.[2]

References

  1. "Definition: 'Cornea Verticillata'". MediLexicon. Retrieved 29 November 2013.
  2. 2.0 2.1 2.2 Chew, E; Ghosh, M; McCulloch, C (June 1982). "Amiodarone-induced cornea verticillata". Canadian journal of ophthalmology. Journal canadien d'ophtalmologie. 17 (3): 96–9. PMID 7116220.
  3. Graff, Jordan M. (February 21, 2005). "Verticillata". University of Iowa Health Care, Ophthalmology and Visual Sciences. Retrieved 29 November 2013.