Multiple endocrine neoplasia type 1 classification: Difference between revisions

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==Overview==
==Overview==
MEN-1 syndrome encompasses enteropancreatic tumors, pituitary adenoma, parathyroid adenoma and other associated tumors such as adrenal cortical tumor, pheochromocytoma, bronchopulmonary NET, thymic NET, gastric NET, lipomas, angiofibromas, collagenomas and meningiomas.
MEN-1 syndrome encompasses enteropancreatic tumors, pituitary adenoma, parathyroid adenoma and other associated tumors such as adrenal cortical tumor, pheochromocytoma, bronchopulmonary (neuro endocrine tumor) NET, thymic NET, gastric NET, lipomas, angiofibromas, collagenomas and meningiomas.


==Classification==
==Classification==

Revision as of 17:01, 6 October 2017

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Aravind Reddy Kothagadi M.B.B.S[2] Ajay Gade MD[3]]

Overview

MEN-1 syndrome encompasses enteropancreatic tumors, pituitary adenoma, parathyroid adenoma and other associated tumors such as adrenal cortical tumor, pheochromocytoma, bronchopulmonary (neuro endocrine tumor) NET, thymic NET, gastric NET, lipomas, angiofibromas, collagenomas and meningiomas.

Classification

  • MEN-1 syndrome encompasses enteropancreatic tumors, pituitary adenoma, parathyroid adenoma and other associated tumors.


Multiple Endocrine Neoplasia-1 (MEN-1) Syndrome Tumors
Enteropancreatic tumor
  • Gastrinoma
  • Insulinoma
  • Glucagonoma
  • Nonfunctioning and PPoma
  • VIPoma
Pituitary adenoma
  • Prolactinoma
  • Somatotrophinoma
  • Corticotropinoma
  • Nonfunctioning
Associated tumors
  • Adrenal cortical tumor
  • Pheochromocytoma
  • Bronchopulmonary NET
  • Thymic NET
  • Gastric NET
  • Lipomas
  • Angiofibromas
  • Collagenomas
  • Meningiomas
Parathyroid adenoma

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