Glycogen storage disease type I surgery: Difference between revisions
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==Surgery== | ==Surgery== | ||
*Liver transplantation may improve the survival of patients with glycogen storage disease type 1. | |||
*Survival rates of patients after liver transplantation are: | |||
==References== | ==References== | ||
Revision as of 21:26, 8 November 2017
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Glycogen storage disease type I Microchapters |
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Differentiating Glycogen storage disease type I from other Diseases |
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Diagnosis |
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Glycogen storage disease type I surgery On the Web |
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief:
Overview
Liver transplantation is the final treatment for patients with metabolic disease associated associated with GSD type 1.
Indications
Indications for liver transplantation include:[1]
- Patients with multifocal
- Growing lesions that do not regress with improved dietary regimens
- Patients who do not have evidence of distant metastatic disease.
Surgery
- Liver transplantation may improve the survival of patients with glycogen storage disease type 1.
- Survival rates of patients after liver transplantation are:
References
- ↑ Kishnani, Priya S.; Austin, Stephanie L.; Abdenur, Jose E.; Arn, Pamela; Bali, Deeksha S.; Boney, Anne; Chung, Wendy K.; Dagli, Aditi I.; Dale, David; Koeberl, Dwight; Somers, Michael J.; Burns Wechsler, Stephanie; Weinstein, David A.; Wolfsdorf, Joseph I.; Watson, Michael S. (2014). "Diagnosis and management of glycogen storage disease type I: a practice guideline of the American College of Medical Genetics and Genomics". Genetics in Medicine. doi:10.1038/gim.2014.128. ISSN 1098-3600.