Diastematomyelia

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Diastematomyelia
ICD-10 Q06.2
ICD-9 742.51
OMIM 222500
DiseasesDB 33901

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Associate Editor-In-Chief: Cafer Zorkun, M.D., Ph.D. [2]


Overview

Diastematomyelia is an uncommon congenital anomaly characterized pathologically by sagittal clefting of the spinal cord or filum terminale, with each half of the spinal cord being surrounded by a dural sac.

This disorder is usually caused by either a fibrous bony septum or an osteocartilaginous septum.

Diastematomyelias are most frequently found in the lumbar spine, followed by the thoracic region.

Some form of an associated congenital anomaly, or dysraphism, of the vertebral column is a constant feature.

Diagnosis

MRI

(Images courtesy of RadsWiki)





See also

  • Diplomyelia


Template:Congenital malformations and deformations of nervous system


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