Desmoid tumor classification

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Desmoid tumor Microchapters

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Patient Information

Overview

Historical Perspective

Classification

Pathophysiology

Causes

Differentiating Desmoid tumor from other Diseases

Epidemiology and Demographics

Risk Factors

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms

Physical Examination

Laboratory Findings

CT

MRI

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Faizan Sheraz, M.D. [2]

Overview

Desmoid tumor may be classified according to etiology into 5 subtypes.[1]

Classification

Desmoid tumor may be classified as follows:[1]

Classification Features

Extraabdominal

Desmoid tumor may involve:

  • Shoulder girdle
  • Trunk
  • Lower extremities

Intraabdominal

Multiple Familial

  • Hereditary predisposition

Gardner Syndrome Associated

Turcot Syndrome Associated

  • Neural tumors

Reference

  1. 1.0 1.1 Economou, Athanasios; Pitta, Xanthi; Andreadis, Efstathios; Papapavlou, Leonidas; Chrissidis, Thomas (2011). "Desmoid tumor of the abdominal wall: a case report". Journal of Medical Case Reports. 5 (1): 326. doi:10.1186/1752-1947-5-326. ISSN 1752-1947.

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