Noncompaction cardiomyopathy echocardiography

Jump to navigation Jump to search

Noncompaction Cardiomyopathy Microchapters

Home

Patient Info

Overview

Historical Perspective

Classification & Nomenclature

Pathophysiology

Genetics
Embryology
Histology
Left Ventricular Dysfunction
Arrhythmias
Thromboembolism
Neuromuscular Disorders

Epidemiology & Demographics

Screening

Natural History, Complications & Prognosis

Differentiating Noncompaction Cardiomyopathy from other Diseases

Diagnosis

History & Symptoms

Physical Examination

Laboratory Studies

Genetic Testing

Electrocardiogram

Holter Monitoring

Chest X Ray

MRI

CT

Echocardiography

Biopsy

Treatment

Medical Therapy

Surgery

Noncompaction cardiomyopathy echocardiography On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

Images

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Noncompaction cardiomyopathy echocardiography

CDC on Noncompaction cardiomyopathy echocardiography

Noncompaction cardiomyopathy echocardiography in the news

Blogs on Noncompaction cardiomyopathy echocardiography

Directions to Hospitals Treating Type page name here

Risk calculators and risk factors for Noncompaction cardiomyopathy echocardiography

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Overview

On echocardiography there is ventricular hypertrophy with deep recesses which tend to be located apically [1].

Echocardiographic findings

  • There are deep trabeculations in the ventricular wall
  • There is systolic dysfunction with an average LVEF of 33% [2]
  • There was diastolic dysfunction in all 17 patients in one series, with 36% of these patients having a restrictie filling pattern[3].
  • The left ventricular wall is thick with a two layered appearance
  • The epicardial layer is compacted and thin and the endocardial layer is non-compacted and thick
  • The ratio of the non-compacted endocardial layer to the epicardial layer is > 2 in adults and >1.4 in children
  • 41% of patients will have involvement of the RV apex [4]

References

  1. Weiford BC, Subbarao VD, Mulhern KM, Noncompaction of the ventricular myocardium. Circulation 109 (24): 2965-71 2004
  2. .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.
  3. .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.
  4. .Oechslin EN, Attenhofer Jost CH, Rojas JR, et al. Long-term follow-up of 34 adults with isolated left ventricular noncompaction: a distinct cardiomyopathy with poor prognosis. J Am Coll Cardiol. 2000; 36: 493–500.

Template:WH Template:WS