Pseudomyxoma peritonei differential diagnosis

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]Associate Editor(s)-in-Chief: Nima Nasiri, M.D.[2]Parminder Dhingra, M.D. [3]

Overview

Pseudomyxoma peritonei must be differentiated from peritoneal carcinomatosis without mucinous ascites, peritoneal sarcomatosis, and peritonitis.

Differential Diagnosis

Pseudomyxoma peritonei must be differentiated from:[1][2]

  • Peritoneal carcinomatosis without mucinous ascites
  • Peritoneal sarcomatosis
  • Peritonitis

Differentiating pseudomyxoma peritonei from other diseases on the basis of [symptom 1], [symptom 2], and [symptom 3]

On the basis bloating, abdominal distention, infertility and hernia , must be differentiated from [disease 1], [disease 2], [disease 3], [disease 4], [disease 5], and [disease 6].

Diseases Clinical manifestations Para-clinical findings Gold standard Additional findings
Symptoms Physical examination
Lab Findings Imaging Histopathology
Symptom 1 Symptom 2 Symptom 3 Physical exam 1 Physical exam 2 Physical exam 3 Lab 1 Lab 2 Lab 3 Imaging 1

CT Scan

Imaging

2

Imaging 3
Pseudomyxoma peritonei
  • Bloating
  • Abdominal distention
  • Abdominal tenderness
  • Low-attenuation
  • Scalloping of the visceral surfaces
Peritoneal carcinomatosis without mucinous ascites
Peritoneal sarcomatosis
Lymphomatosis
  • CD20, CD79a, CD10
  • Thickened peritoneal surfaces.
  • Multifocal nodules and masses
  • Atypical lymphoid cells
Tuberclousis Peritonitis
  • Caseating granuloma with central area of necrotic acellular debris surrounded by histiocytes
Endometriosis
Sclerosing encapsulating peritonitis
Gliomatosis Peritonei
Osseous metaplasia
Splenosis
Melanosis
Inflammatory Pseudotumor

References

  1. Harmon RL, Sugarbaker PH (February 2005). "Prognostic indicators in peritoneal carcinomatosis from gastrointestinal cancer". Int Semin Surg Oncol. 2 (1): 3. doi:10.1186/1477-7800-2-3. PMC 549516. PMID 15701175.
  2. Carr NJ, Bibeau F, Bradley RF, Dartigues P, Feakins RM, Geisinger KR, Gui X, Isaac S, Milione M, Misdraji J, Pai RK, Rodriguez-Justo M, Sobin LH, van Velthuysen MF, Yantiss RK (December 2017). "The histopathological classification, diagnosis and differential diagnosis of mucinous appendiceal neoplasms, appendiceal adenocarcinomas and pseudomyxoma peritonei". Histopathology. 71 (6): 847–858. doi:10.1111/his.13324. PMID 28746986.

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