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{| class="wikitable"
<table class="wikitable">
<tr class="v-firstrow"><th>Drug</th><th>Clinical course</th><th>Stable</th></tr>
<tr><td>Physical examination</td><td> No evidence of heart failure</td></tr>
<tr><td>Functional class</td><td> I/II</td></tr>
<tr><td>6MWD</td><td> Greater than 400 m</td></tr>
<tr><td>Echocardiogram</td><td>RV size normal</td></tr>


|-
<tr><td>Hemodynamics</td><td>RAP normal <br> CI normal</td></tr>


! Drug 
<tr><td>BNP</td><td>Near normal or stable</td></tr>


! Route of administration
<tr><td>Treatment</td><td>Oral therapy</td></tr>


! Dose titration
<tr><td>Frequency of evaluation </td><td>Q 3 to Q 6 months</td></tr>


! Dose range
<tr><td>FC assessment</td><td> Every clinic visit </td></tr>


! Side effects
<tr><td>6MWT</td><td> Every clinic visit</td></tr>


|-
<tr><td>Echocardiogram<sup>2</sup></td><td>Q 12 months/center dependent</td></tr>
| Epoprostenol


| Intravenous infusion
<tr><td>BNP</td><td>center dependent</td></tr>


| 2 ng/kg/min every 10 to 15 min
<tr><td>RHC</td><td>Clinical deterioration and center dependent</td></tr>


| 2 to 10 ng/kg/min
</table>


| Headache, nausea, lightheadedness


|-
<table class="wikitable">
 
<tr class="v-firstrow"><th>Drug</th><th>Clinical course</th><th>Unstable</th></tr>
| Adenosine
<tr><td>Physical examination</td><td> Signs of heart failure</td></tr>
 
<tr><td>Functional class</td><td> IV</td></tr>
 
<tr><td>6MWD</td><td> Less than 400 m</td></tr>
| Intravenous infusion
<tr><td>Echocardiogram</td><td>RV Enlargement</td></tr>
 
<tr><td>Hemodynamics</td><td>RAP high <br> CI low</td></tr>
 
<tr><td>BNP</td><td>Elevated/Increasing</td></tr>
| 50 mcg/kg/min every 2 min
<tr><td>Treatment</td><td>Intravenous prostacyclin and/or combination treatment</td></tr>
 
<tr><td>Frequency of evaluation </td><td>Q 1 to Q 3 months</td></tr>
 
<tr><td>FC assessment</td><td> Every clinic visit </td></tr>
| 50 to 250 mcg/kg/min
<tr><td>6MWT</td><td> Every clinic visit</td></tr>
 
<tr><td>Echocardiogram<sup>2</sup></td><td>Q 6 to Q 12 months/center dependent</td></tr>
 
<tr><td>BNP</td><td>center dependent</td></tr>
| Dyspnea, chest pain, AV block
<tr><td>RHC</td><td>Q 6 to Q 12 months or clinical deterioration</td></tr>
 
</table>
 
|-
 
| Nitric Oxide
 
 
| Inhaled
 
 
| None
 
 
| 10 to 80 ppm
 
| Increased left heart filling pressure in susceptible patients
 
|-
 
|}

Revision as of 19:28, 9 January 2014

DrugClinical courseStable
Physical examination No evidence of heart failure
Functional class I/II
6MWD Greater than 400 m
EchocardiogramRV size normal
HemodynamicsRAP normal
CI normal
BNPNear normal or stable
TreatmentOral therapy
Frequency of evaluation Q 3 to Q 6 months
FC assessment Every clinic visit
6MWT Every clinic visit
Echocardiogram2Q 12 months/center dependent
BNPcenter dependent
RHCClinical deterioration and center dependent


DrugClinical courseUnstable
Physical examination Signs of heart failure
Functional class IV
6MWD Less than 400 m
EchocardiogramRV Enlargement
HemodynamicsRAP high
CI low
BNPElevated/Increasing
TreatmentIntravenous prostacyclin and/or combination treatment
Frequency of evaluation Q 1 to Q 3 months
FC assessment Every clinic visit
6MWT Every clinic visit
Echocardiogram2Q 6 to Q 12 months/center dependent
BNPcenter dependent
RHCQ 6 to Q 12 months or clinical deterioration