Rhabdomyosarcoma classification: Difference between revisions
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==Overview== | ==Overview== | ||
Rhabdomyosarcoma may be classified according to the "International classification of rhabdomyosarcoma" into six subtypes Alveolar rhabdomyosarcoma, embryonal rhabdomyosarcoma, botryoid rhabdomyosarcoma, spindle cell rhabdomyosarcoma, and undifferentiated rhabdomyosarcoma. | Rhabdomyosarcoma may be classified according to the "International classification of rhabdomyosarcoma" into six subtypes: Alveolar rhabdomyosarcoma, embryonal rhabdomyosarcoma, botryoid rhabdomyosarcoma, spindle cell rhabdomyosarcoma, and undifferentiated rhabdomyosarcoma. | ||
==Classification== | ==Classification== |
Revision as of 14:48, 11 September 2015
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1];Associate Editor(s)-in-Chief: Suveenkrishna Pothuru, M.B,B.S. [2]
Overview
Rhabdomyosarcoma may be classified according to the "International classification of rhabdomyosarcoma" into six subtypes: Alveolar rhabdomyosarcoma, embryonal rhabdomyosarcoma, botryoid rhabdomyosarcoma, spindle cell rhabdomyosarcoma, and undifferentiated rhabdomyosarcoma.
Classification
Multiple classification systems have been proposed for subclassifying rhabdomyosarcomas. The most recent classification system, the "International classification of rhabdomyosarcoma", was created by the Intergroup Rhabdomyosarcoma Study.[1] This system attempts to combine elements of the previous systems and correlate these with prognosis based on tumor type. Rhabdomyosarcomas classified into six subtypes:
- Alveolar rhabdomyosarcoma
- Usually affects young adults
- Early metastasis is common
- Usually arises in regions with skeletal muscle
- Embryonal rhabdomyosarcoma
- Usually affects children younger than 10 Years of age
- Typically locally invasive
- Usually arises in regions without skeletal muscle
- Botryoid rhabdomyosarcoma
- Spindle cell rhabdomyosarcoma
- Undifferentiated sarcoma
Several additional subtypes of rhabdomyosarcoma exist that do not fit into the International Classification scheme:
- Pleomorphic rhabdomyosarcoma: Usually occurs in adults rather than children
- Sclerosing rhabdomyosarcoma: It is a rare rhabdomyosarcoma subtype
References
- ↑ Newton WA, Gehan EA, Webber BL; et al. (September 1995). "Classification of rhabdomyosarcomas and related sarcomas. Pathologic aspects and proposal for a new classification—an Intergroup Rhabdomyosarcoma Study". Cancer. 76 (6): 1073–85. doi:10.1002/1097-0142(19950915)76:6<1073::AID-CNCR2820760624>3.0.CO;2-L. PMID 8625211.