Restrictive cardiomyopathy: Difference between revisions

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{|style="width:80%; height:100px" border="1"
{|style="width:80%; height:100px" border="1"
|style="height:100px"; style="width:25%" border="1" bgcolor="LightSteelBlue" |'''Cardiovascular'''
|style="height:100px"; style="width:25%" border="1" bgcolor="LightSteelBlue" |'''Cardiovascular'''
|style="height:100px"; style="width:75%" border="1" bgcolor="Beige" | No underlying causes
|style="height:100px"; style="width:75%" border="1" bgcolor="Beige" | [[Amyloidosis]], [[carcinoid syndrome|carcinoid heart disease]], [[cardiac amyloidosis]], [[endocardial fibroelastosis]], [[endomyocardial fibrosis]], [[heart transplant]], [[hemochromatosis]], [[Hurler syndrome]], [[Noonan's syndrome]]
|-
|-
|bgcolor="LightSteelBlue"| '''Chemical/Poisoning'''
|bgcolor="LightSteelBlue"| '''Chemical/Poisoning'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[mercury|Mercurial agents]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Dermatologic'''
| '''Dermatologic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Drug Side Effect'''
| '''Drug Side Effect'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Anthracyclines]], [[busulfan]], [[chemotherapy]], [[drugs]], [[ergotamine]], [[hydroxychloroquine]], [[methysergide]], [[serotonin]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Endocrine'''
| '''Endocrine'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Amyloidosis]], [[carcinoid syndrome]], [[carcinoid tumors]], [[diabetes mellitus]],  [[carcinoid syndrome|carcinoid heart disease]], [[hemochromatosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Gastroenterologic'''
| '''Gastroenterologic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Alpha-L-iduronidase deficiency]], [[glycogen storage disease]], [[hemochromatosis]], [[Hurler syndrome]], [[sarcoidosis]], [[carcinoid syndrome|carcinoid heart disease]], [[carcinoid syndrome]], [[scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Genetic'''
| '''Genetic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Alpha-L-iduronidase deficiency]], [[Anderson-Fabry disease]], [[cystinosis]], [[desminopathy]], [[Fabry's disease]], [[familial]], [[Gaucher's disease]], [[hemochromatosis]], [[Hurler syndrome]], [[mucopolysaccharidosis]], [[Noonan's syndrome]], [[pseudoxanthoma elasticum]], sarcomeric protein mutations, [[Werner's syndrome]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Hematologic'''
| '''Hematologic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[carcinoid syndrome|Carcinoid heart disease]], [[carcinoid syndrome]], [[carcinoid tumors]], [[Gaucher's disease]], [[hemochromatosis]], [[Hypereosinophilic syndrome]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Iatrogenic'''
| '''Iatrogenic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[radiotherapy|Postirradiation fibrosis]], [[Radiation]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Infectious Disease'''
| '''Infectious Disease'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Loeffler's syndrome]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Musculoskeletal/Orthopedic'''
| '''Musculoskeletal/Orthopedic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Hemochromatosis]], [[scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Nutritional/Metabolic'''
| '''Nutritional/Metabolic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Alpha-L-iduronidase deficiency]], [[amyloidosis]], [[Anderson-Fabry disease]], [[cystinosis]], [[Fabry's disease]], fatty infiltration, [[Gaucher's disease]], [[generalized gangliosidosis GM1]], [[glycogen storage disease]], [[Hurler syndrome]], [[I-cell disease]], [[mucolipidosis II alpha/beta]], [[mucopolysaccharidosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Oncologic'''
| '''Oncologic'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[carcinoid syndrome|Carcinoid heart disease]], [[carcinoid syndrome]], [[carcinoid tumors]], [[hypereosinophilic syndrome]], [[lymphoma]], [[malignancy]], [[metastasis|metastatic cancers]], [[paraneoplastic syndrome]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Psychiatric'''
| '''Psychiatric'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Hurler syndrome]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Pulmonary'''
| '''Pulmonary'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Churg-Strauss syndrome]], [[Loeffler's syndrome]], [[sarcoidosis]], [[scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Renal/Electrolyte'''
| '''Renal/Electrolyte'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
| '''Rheumatology/Immunology/Allergy'''
| '''Rheumatology/Immunology/Allergy'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Amyloidosis]], [[cardiac amyloidosis]], [[Churg-Strauss syndrome]], [[Loeffler's syndrome]], [[paraneoplastic syndrome]], [[reactive arthritis]], [[sarcoidosis]], [[scleroderma]], [[systemic sclerosis]]
|-
|-
|-bgcolor="LightSteelBlue"
|-bgcolor="LightSteelBlue"
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|-bgcolor="LightSteelBlue"
| '''Miscellaneous'''
| '''Miscellaneous'''
|bgcolor="Beige"| No underlying causes
|bgcolor="Beige"| [[Idiopathic]]
|-
|-
|}
|}

Revision as of 05:04, 27 October 2014

WikiDoc Resources for Restrictive cardiomyopathy

Articles

Most recent articles on Restrictive cardiomyopathy

Most cited articles on Restrictive cardiomyopathy

Review articles on Restrictive cardiomyopathy

Articles on Restrictive cardiomyopathy in N Eng J Med, Lancet, BMJ

Media

Powerpoint slides on Restrictive cardiomyopathy

Images of Restrictive cardiomyopathy

Photos of Restrictive cardiomyopathy

Podcasts & MP3s on Restrictive cardiomyopathy

Videos on Restrictive cardiomyopathy

Evidence Based Medicine

Cochrane Collaboration on Restrictive cardiomyopathy

Bandolier on Restrictive cardiomyopathy

TRIP on Restrictive cardiomyopathy

Clinical Trials

Ongoing Trials on Restrictive cardiomyopathy at Clinical Trials.gov

Trial results on Restrictive cardiomyopathy

Clinical Trials on Restrictive cardiomyopathy at Google

Guidelines / Policies / Govt

US National Guidelines Clearinghouse on Restrictive cardiomyopathy

NICE Guidance on Restrictive cardiomyopathy

NHS PRODIGY Guidance

FDA on Restrictive cardiomyopathy

CDC on Restrictive cardiomyopathy

Books

Books on Restrictive cardiomyopathy

News

Restrictive cardiomyopathy in the news

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News trends on Restrictive cardiomyopathy

Commentary

Blogs on Restrictive cardiomyopathy

Definitions

Definitions of Restrictive cardiomyopathy

Patient Resources / Community

Patient resources on Restrictive cardiomyopathy

Discussion groups on Restrictive cardiomyopathy

Patient Handouts on Restrictive cardiomyopathy

Directions to Hospitals Treating Restrictive cardiomyopathy

Risk calculators and risk factors for Restrictive cardiomyopathy

Healthcare Provider Resources

Symptoms of Restrictive cardiomyopathy

Causes & Risk Factors for Restrictive cardiomyopathy

Diagnostic studies for Restrictive cardiomyopathy

Treatment of Restrictive cardiomyopathy

Continuing Medical Education (CME)

CME Programs on Restrictive cardiomyopathy

International

Restrictive cardiomyopathy en Espanol

Restrictive cardiomyopathy en Francais

Business

Restrictive cardiomyopathy in the Marketplace

Patents on Restrictive cardiomyopathy

Experimental / Informatics

List of terms related to Restrictive cardiomyopathy

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Synonyms and keywords: Infiltrative cardiomyopathy; RCM

Overview

Restrictive cardiomyopathy is the least common cardiomyopathy. It is called this because it restricts the heart from stretching and filling with blood properly. Rhythmicity and contractility of the heart may be normal, but the stiff walls of the heart chambers (atria and ventricles) keep them from adequately filling. So blood flow is reduced, and blood that would normally enter the heart is backed up in the circulatory system. In time, restrictive cardiomyopathy patients develop heart failure.

Causes

Life Threatening Causes

Life-threatening causes include conditions which may result in death or permanent disability within 24 hours if left untreated.

Common Causes

Causes by Organ System

Cardiovascular Amyloidosis, carcinoid heart disease, cardiac amyloidosis, endocardial fibroelastosis, endomyocardial fibrosis, heart transplant, hemochromatosis, Hurler syndrome, Noonan's syndrome
Chemical/Poisoning Mercurial agents
Dental No underlying causes
Dermatologic Scleroderma, systemic sclerosis
Drug Side Effect Anthracyclines, busulfan, chemotherapy, drugs, ergotamine, hydroxychloroquine, methysergide, serotonin
Ear Nose Throat No underlying causes
Endocrine Amyloidosis, carcinoid syndrome, carcinoid tumors, diabetes mellitus, carcinoid heart disease, hemochromatosis
Environmental No underlying causes
Gastroenterologic Alpha-L-iduronidase deficiency, glycogen storage disease, hemochromatosis, Hurler syndrome, sarcoidosis, carcinoid heart disease, carcinoid syndrome, scleroderma, systemic sclerosis
Genetic Alpha-L-iduronidase deficiency, Anderson-Fabry disease, cystinosis, desminopathy, Fabry's disease, familial, Gaucher's disease, hemochromatosis, Hurler syndrome, mucopolysaccharidosis, Noonan's syndrome, pseudoxanthoma elasticum, sarcomeric protein mutations, Werner's syndrome
Hematologic Carcinoid heart disease, carcinoid syndrome, carcinoid tumors, Gaucher's disease, hemochromatosis, Hypereosinophilic syndrome
Iatrogenic Postirradiation fibrosis, Radiation
Infectious Disease Loeffler's syndrome
Musculoskeletal/Orthopedic Hemochromatosis, scleroderma, systemic sclerosis
Neurologic No underlying causes
Nutritional/Metabolic Alpha-L-iduronidase deficiency, amyloidosis, Anderson-Fabry disease, cystinosis, Fabry's disease, fatty infiltration, Gaucher's disease, generalized gangliosidosis GM1, glycogen storage disease, Hurler syndrome, I-cell disease, mucolipidosis II alpha/beta, mucopolysaccharidosis
Obstetric/Gynecologic No underlying causes
Oncologic Carcinoid heart disease, carcinoid syndrome, carcinoid tumors, hypereosinophilic syndrome, lymphoma, malignancy, metastatic cancers, paraneoplastic syndrome
Ophthalmologic No underlying causes
Overdose/Toxicity No underlying causes
Psychiatric Hurler syndrome
Pulmonary Churg-Strauss syndrome, Loeffler's syndrome, sarcoidosis, scleroderma, systemic sclerosis
Renal/Electrolyte Scleroderma, systemic sclerosis
Rheumatology/Immunology/Allergy Amyloidosis, cardiac amyloidosis, Churg-Strauss syndrome, Loeffler's syndrome, paraneoplastic syndrome, reactive arthritis, sarcoidosis, scleroderma, systemic sclerosis
Sexual No underlying causes
Trauma No underlying causes
Urologic No underlying causes
Miscellaneous Idiopathic

Causes in Alphabetical Order

Diagnosis

Electrocardiogram

Shown below is an example of restrictive cardiomyopathy with low voltage and flipped anterior T waves.

References


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