Pityriasis rubra pilaris: Difference between revisions

	Pityriasis rubra pilaris;
ICD-10	L44.0
ICD-9	696.4
OMIM	173200
DiseasesDB	29305
MedlinePlus	001471
eMedicine	derm/337
MeSH	D010916

VisualWikitext

Revision as of 21:07, 24 September 2014

Template:Search infobox Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Kiran Singh, M.D. [2]

Overview

Pityriasis rubra pilaris (PRP) is a rare and chronic skin disorder that often has a sudden onset. Symptoms may include reddish-orange patches (Latin: rubra) on the skin, severe flaking (Latin: pityriasis), uncomfortable itching, thickening of the skin on the feet and hands, and thickened bumps around hair follicles (Latin: pilus for hair). For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body. PRP has a varied clinical progression and a varied rate of improvement. There is no known cause or cure.

It was first described by Marie-Guillaume-Alphonse Devergie in 1856,^[1] and the condition is also known as Devergie's disease.^[2]

Classification

Dr. W.A.D. Griffiths, from Great Britain, classified six forms of PRP in the early 1980s.^[3] At this time, the causes of PRP are still unknown and symptoms can be difficult to diagnose. Frequently, more than one medical professional will be consulted before an accurate PRP diagnosis is made.

Dermatologists have identified both an acquired form and an inherited form (familial) of PRP and have described them in medical journals. The acquired form usually shows a spontaneous or gradual remission of symptoms within several years although long-term symptoms may continue for years. The inherited form starts early in childhood with persistent long-term symptoms into adulthood.

Although most people who develop PRP are over age 50, individuals of any age, race, and nationality can be affected. Women and men seem to be equally affected.

Diagnosis

Physical Examination

Skin

Trunk

Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.[4]

Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]
Pityriasis rubra pilaris. Adapted from Dermatology Atlas.^[4]

Extremities

Neck

File:=====Ear=====

Gluteal Region

References

↑ Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)". Gazette hebdomadaire de médecine et de chirurgie, Paris (in French). 3: 197–201.
↑ Template:WhoNamedIt2 and the eponymous named Template:WhoNamedIt
↑ "Pityriasis rubra pilaris". DermNZ (New Zealand Dermatological Society). 26 Dec 2006. Retrieved 2007-05-08. - describes the various forms
↑ ^4.00 ^4.01 ^4.02 ^4.03 ^4.04 ^4.05 ^4.06 ^4.07 ^4.08 ^4.09 ^4.10 ^4.11 ^4.12 ^4.13 ^4.14 ^4.15 ^4.16 ^4.17 ^4.18 ^4.19 ^4.20 ^4.21 ^4.22 ^4.23 ^4.24 ^4.25 ^4.26 ^4.27 ^4.28 ^4.29 ^4.30 ^4.31 ^4.32 ^4.33 ^4.34 ^4.35 ^4.36 ^4.37 ^4.38 ^4.39 ^4.40 ^4.41 ^4.42 ^4.43 ^4.44 ^4.45 ^4.46 ^4.47 ^4.48 ^4.49 ^4.50 ^4.51 ^4.52 ^4.53 ^4.54 ^4.55 ^4.56 ^4.57 ^4.58 ^4.59 ^4.60 ^4.61 ^4.62 ^4.63 ^4.64 ^4.65 ^4.66 ^4.67 ^4.68 ^4.69 ^4.70 ^4.71 ^4.72 ^4.73 ^4.74 ^4.75 ^4.76 ^4.77 ^4.78 ^4.79 ^4.80 ^4.81 ^4.82 ^4.83 ^4.84 ^4.85 ^4.86 ^4.87 ^4.88 ^4.89 ^4.90 ^4.91 ^4.92 ^4.93 ^4.94 "Dermatology Atlas".

External links

PRP Support Group - information regarding day-to-day care and medical treatment and having an international membership.
skin diseases Information
Dr. Griffith (June 1998). Editors Champion R.H., Burton J.L., Burns D.A. and Breathnach S.M., ed. Textbook of Dermatology. 2 (6th edition ed.). pp. 1539–1545. ISBN 0632050640. Unknown parameter |chaper= ignored (help)

de:Pityriasis rubra pilaris Template:SIB

Template:WikiDoc Sources

[1] Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)". Gazette hebdomadaire de médecine et de chirurgie, Paris (in French). 3: 197–201.

[2] Template:WhoNamedIt2 and the eponymous named Template:WhoNamedIt

[3] "Pityriasis rubra pilaris". DermNZ (New Zealand Dermatological Society). 26 Dec 2006. Retrieved 2007-05-08. - describes the various forms

[Dermatology_Atlas-4] 4.00 ^4.01 ^4.02 ^4.03 ^4.04 ^4.05 ^4.06 ^4.07 ^4.08 ^4.09 ^4.10 ^4.11 ^4.12 ^4.13 ^4.14 ^4.15 ^4.16 ^4.17 ^4.18 ^4.19 ^4.20 ^4.21 ^4.22 ^4.23 ^4.24 ^4.25 ^4.26 ^4.27 ^4.28 ^4.29 ^4.30 ^4.31 ^4.32 ^4.33 ^4.34 ^4.35 ^4.36 ^4.37 ^4.38 ^4.39 ^4.40 ^4.41 ^4.42 ^4.43 ^4.44 ^4.45 ^4.46 ^4.47 ^4.48 ^4.49 ^4.50 ^4.51 ^4.52 ^4.53 ^4.54 ^4.55 ^4.56 ^4.57 ^4.58 ^4.59 ^4.60 ^4.61 ^4.62 ^4.63 ^4.64 ^4.65 ^4.66 ^4.67 ^4.68 ^4.69 ^4.70 ^4.71 ^4.72 ^4.73 ^4.74 ^4.75 ^4.76 ^4.77 ^4.78 ^4.79 ^4.80 ^4.81 ^4.82 ^4.83 ^4.84 ^4.85 ^4.86 ^4.87 ^4.88 ^4.89 ^4.90 ^4.91 ^4.92 ^4.93 ^4.94 "Dermatology Atlas".

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v t e Diseases of the skin and subcutaneous tissue (integumentary system) (L, 680-709)
Infections	Template:Navbox subgroup
Bullous disorders	acantholysis (Pemphigus, Transient acantholytic dermatosis) · Pemphigoid (Bullous, Cicatricial, Gestational) · Dermatitis herpetiformis
Inflammatory	Template:Navbox subgroup
Radiation-related disorders	Sunburn · actinic rays (Actinic keratosis, Actinic cheilitis) · Polymorphous light eruption (Acne aestivalis) · Radiodermatitis · Erythema ab igne
Pigmentation disorder	hypopigmentation (Albinism, Vitiligo) · hyperpigmentation (Melasma, Freckle, Café au lait spot, Lentigo/Liver spot, Acanthosis nigricans, Acral acanthotic anomaly)
Other skin	keratosis/hyperkeratosis (Seborrheic keratosis, Callus) · other epidermal thickening (Ichthyosis acquisita, Palmoplantar keratoderma) skin ulcer (Pyoderma gangrenosum, Bedsore) Cutaneous Markers of Internal Malignancy (Florid cutaneous papillomatosis, acanthosis nigricans, sign of Leser-Trelat) atrophic (Lichen sclerosus, Acrodermatitis chronica atrophicans) necrobiosis (Granuloma annulare, Necrobiosis lipoidica) · other granuloma (Granuloma faciale, Pyogenic granuloma) cutaneous vasculitis (Livedoid vasculitis, Erythema elevatum diutinum)
Connective tissues	collagen disease: Keloid localized connective tissue disorders: Lupus erythematosus (Discoid lupus erythematosus, Subacute cutaneous lupus erythematosus) · Scleroderma/Morphea · Linear scleroderma · Calcinosis cutis · Sclerodactyly · Ainhum
see also congenital, neoplasia