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| {{DiseaseDisorder infobox |
| | #REDIRECT [[Langerhans cell histiocytosis]] |
| Name = {{PAGENAME}} |
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| ICD10 = {{ICD10|C|96|0|c|81}} |
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| ICD9 = {{ICD9|202.5}} |
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| ICDO = |
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| Image = |
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| Caption = |
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| OMIM = 246400 |
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| MedlinePlus = |
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| eMedicineSubj = |
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| eMedicineTopic = |
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| DiseasesDB = 5906 |
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| MeshID = D006646 |
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| }}
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| {{SI}}
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| {{CMG}}
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| {{EH}}
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| '''Letterer-Siwe disease''' is a condition where [[histiocytes]] proliferate in the body. It is sometimes classified as a form of [[Langerhans cell histiocytosis]], or as a disseminated form of [[histiocytosis X]]. It is most commonly seen in children less than two years old.
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| Symptoms include [[lymphadenopathy]], [[hepatosplenomegaly]], and [[seborrhea]]-like lesions on the skin. Untreated, the disease is fatal. The five-year survival rate with treatment is fifty percent.
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| ==External links==
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| * {{WhoNamedIt|synd|1648}}
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| * {{Chorus|00230}}
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| * [http://www.5mcc.com/Assets/SUMMARY/TP0529.html 5mcc]
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| * {{DermNet|dermal-infiltrative/langerhans}}
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| ==See also==
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| *[[Histiocytosis]]
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| {{SIB}}
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| [[es:Enfermedad de Letterer-Siwe]]
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| [[pl:Choroba Abta-Letterera-Siwe'go]]
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| {{WH}}
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| {{WS}}
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| [[Category:Disease]]
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| [[Category:Hematology]]
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