Erdheim-Chester disease: Difference between revisions

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{{CMG}}
{{CMG}}


{{SK}} Erdheim-Chester syndrome; polyostotic sclerosing histiocytosis
{{SK}} Erdheim-Chester syndrome; polyostotic sclerosing histiocytosis; ECD


==Overview==
==[[Erdheim-Chester disease overview|Overview]]==


==History==
==[[Erdheim-Chester disease historical perspective|Historical Perspective]]==


==Clinical Presentation==
==[[Erdheim-Chester disease pathophysiology|Pathophysiology]]==


==Histology==
==[[Erdheim-Chester disease causes|Causes]]==
 
==[[Erdheim-Chester disease differential diagnosis|Differentiating Erdheim-Chester disease from other Diseases]]==
 
==[[Erdheim-Chester disease epidemiology and demographics|Epidemiology and Demographics]]==
 
==[[Erdheim-Chester disease natural history, complications and prognosis|Natural History, Complications and Prognosis]]==


==Diagnosis==
==Diagnosis==
 
[[Erdheim-Chester disease history and symptoms|History and Symptoms]] | [[Erdheim-Chester disease physical examination|Physical Examination]] | [[Erdheim-Chester disease laboratory findings|Laboratory Findings]] |  [[Erdheim-Chester disease electrocardiogram|Electrocardiogram]] | [[Erdheim-Chester disease x ray|X Ray]] | [[Erdheim-Chester disease CT|CT]] | [[Erdheim-Chester disease MRI|MRI]] | [[Erdheim-Chester disease echocardiography or ultrasound|Echocardiography or Ultrasound]] | [[Erdheim-Chester disease other imaging findings|Other Imaging Findings]] | [[Erdheim-Chester disease other diagnostic studies|Other Diagnostic Studies]]
ECD is not a common cause of exophthalmos but can be diagnosed by biopsy.  However, like all biopsies, this may be inconclusive.<ref name="Mdanderson"> {{cite web |url=http://www.mdanderson.org/diseases/eyecancer/display.cfm?id=5423a04c-459e-4e12-a737309ef2e1e299&method=displayfull |title=Erdheim Chester Disease - M. D. Anderson Cancer Center |accessdate=2007-08-26 |format= |work=}}</ref>


==Treatment==
==Treatment==
[[Erdheim-Chester disease medical therapy|Medical Therapy]] | [[Erdheim-Chester disease surgery|Surgery]] | [[Erdheim-Chester disease cost-effectiveness of therapy|Cost-Effectiveness of Therapy]] | [[Erdheim-Chester disease future or investigational therapies|Future or Investigational Therapies]]
<!-- Use the following categories
==Prognosis==
==Further Reading==
==External Links==
-->


==References==
==Case Studies==
{{Reflist|2}}
[[Erdheim-Chester disease case study one|Case #1]]


{{Hematology}}
{{Hematology}}

Latest revision as of 19:36, 21 September 2012

Erdheim-Chester disease
ICD-10 C96.1
ICD-9 202.3
DiseasesDB 29792
MeSH D031249

Erdheim-Chester disease Microchapters

Home

Patient Information

Overview

Historical Perspective

Pathophysiology

Causes

Differentiating Erdheim-Chester disease from other Diseases

Epidemiology and Demographics

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms

Physical Examination

Laboratory Findings

Electrocardiogram

X Ray

CT

MRI

Echocardiography or Ultrasound

Other Imaging Findings

Other Diagnostic Studies

Treatment

Medical Therapy

Surgery

Cost-Effectiveness of Therapy

Future or Investigational Therapies

Case Studies

Case #1

Erdheim-Chester disease On the Web

Most recent articles

Most cited articles

Review articles

CME Programs

Powerpoint slides

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American Roentgen Ray Society Images of Erdheim-Chester disease

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X-rays
Echo & Ultrasound
CT Images
MRI

Ongoing Trials at Clinical Trials.gov

US National Guidelines Clearinghouse

NICE Guidance

FDA on Erdheim-Chester disease

CDC on Erdheim-Chester disease

Erdheim-Chester disease in the news

Blogs on Erdheim-Chester disease

Directions to Hospitals Treating Erdheim-Chester disease

Risk calculators and risk factors for Erdheim-Chester disease

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]

Synonyms and keywords: Erdheim-Chester syndrome; polyostotic sclerosing histiocytosis; ECD

Overview

Historical Perspective

Pathophysiology

Causes

Differentiating Erdheim-Chester disease from other Diseases

Epidemiology and Demographics

Natural History, Complications and Prognosis

Diagnosis

History and Symptoms | Physical Examination | Laboratory Findings | Electrocardiogram | X Ray | CT | MRI | Echocardiography or Ultrasound | Other Imaging Findings | Other Diagnostic Studies

Treatment

Medical Therapy | Surgery | Cost-Effectiveness of Therapy | Future or Investigational Therapies

Case Studies

Case #1

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