Craniopharyngioma

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Overview

Craniopharyngioma is a type of tumor that comprises 9% of all pediatric brain tumors. They usually occur in children between 5 and 10 years of age.^[1]

It has a point prevalence of approximately 2/100,000.^[2]

They are also known as Rathke pouch tumors, hypophyseal duct tumors, or adamantinomas.

Presentation

They are very slow growing tumors. They arise from the cells along the pituitary stalk. They are classified as benign.^[3]

Craniopharyngioma is a rare, usually suprasellar^[4] neoplasm, which may be cystic, that develops from the nests of epithelium derived from Rathke's pouch.

Histology

The histologic pattern consists of nesting of squamous epithelium bordered by radially arranged cells. It is frequently accompanied by calcium deposition and have a microscopic papillary architecture.

Possible symptoms

Diagnostic Findings

MRI

(Images courtesy of RadsWiki)

Craniopharyngioma
Craniopharyngioma
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Craniopharyngioma
Craniopharyngioma

References

↑ Hamid R, Sarkar S, Hossain MA, Mazumder U, Akanda NI, Parvin R (2007). "Clinical picture of craniopharyngioma in childhood". Mymensingh medical journal : MMJ. 16 (2): 123–6. PMID 17703145.
↑ Garnett MR, Puget S, Grill J, Sainte-Rose C (2007). "Craniopharyngioma". Orphanet journal of rare diseases. 2: 18. doi:10.1186/1750-1172-2-18. PMID 17425791.
↑ Garrè ML, Cama A (2007). "Craniopharyngioma: modern concepts in pathogenesis and treatment". Curr. Opin. Pediatr. 19 (4): 471–9. doi:10.1097/MOP.0b013e3282495a22. PMID 17630614.
↑ Rodriguez FJ, Scheithauer BW, Tsunoda S, Kovacs K, Vidal S, Piepgras DG (2007). "The spectrum of malignancy in craniopharyngioma". Am. J. Surg. Pathol. 31 (7): 1020–8. doi:10.1097/PAS.0b013e31802d8a96. PMID 17592268.

External links

Template:Nervous tissue tumors Template:SIB de:Kraniopharyngeom

Template:WikiDoc Sources

[pmid17703145-1] Hamid R, Sarkar S, Hossain MA, Mazumder U, Akanda NI, Parvin R (2007). "Clinical picture of craniopharyngioma in childhood". Mymensingh medical journal : MMJ. 16 (2): 123–6. PMID 17703145.

[pmid17425791-2] Garnett MR, Puget S, Grill J, Sainte-Rose C (2007). "Craniopharyngioma". Orphanet journal of rare diseases. 2: 18. doi:10.1186/1750-1172-2-18. PMID 17425791.

[pmid17630614-3] Garrè ML, Cama A (2007). "Craniopharyngioma: modern concepts in pathogenesis and treatment". Curr. Opin. Pediatr. 19 (4): 471–9. doi:10.1097/MOP.0b013e3282495a22. PMID 17630614.

[pmid17592268-4] Rodriguez FJ, Scheithauer BW, Tsunoda S, Kovacs K, Vidal S, Piepgras DG (2007). "The spectrum of malignancy in craniopharyngioma". Am. J. Surg. Pathol. 31 (7): 1020–8. doi:10.1097/PAS.0b013e31802d8a96. PMID 17592268.

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