Congenital adrenal hyperplasia surgery: Difference between revisions

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{{Congenital adrenal hyperplasia}}
{{Congenital adrenal hyperplasia}}
 
{{CMG}} {{AE}} {{MAD}}
== Overview ==
== Overview ==
Reconstructive surgery and Surgical adrenalectomy  
Reconstructive surgery and Surgical adrenalectomy.
 
== Surgery ==
== Surgery ==
=== '''Reconstructive surgery''' ===
=== '''Reconstructive surgery''' ===
reconstructive gynecologic surgery as adolescents or adults, including clitoroplasty and vaginoplasty. 39
reconstructive gynecologic surgery as adolescents or adults, including clitoroplasty and vaginoplasty.<ref name="pmid9156043">{{cite journal| author=Premawardhana LD, Hughes IA, Read GF, Scanlon MF| title=Longer term outcome in females with congenital adrenal hyperplasia (CAH): the Cardiff experience. | journal=Clin Endocrinol (Oxf) | year= 1997 | volume= 46 | issue= 3 | pages= 327-32 | pmid=9156043 | doi= | pmc= | url=https://www.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pubmed&tool=sumsearch.org/cite&retmode=ref&cmd=prlinks&id=9156043  }}</ref>
 
==== '''Surgical adrenalectomy''' ====
==== '''Surgical adrenalectomy''' ====
The major benefit is lowering adrenal androgen and progesterone secretion. However,It increases dependency on glucocorticoid and mineralocorticoid replacement therapy.  [29].
The major benefit is lowering adrenal androgen and progesterone secretion. However, It increases dependency on glucocorticoid and mineralocorticoid replacement therapy.<ref name="pmid22904181">{{cite journal| author=Crocker MK, Barak S, Millo CM, Beall SA, Niyyati M, Chang R et al.| title=Use of PET/CT with cosyntropin stimulation to identify and localize adrenal rest tissue following adrenalectomy in a woman with congenital adrenal hyperplasia. | journal=J Clin Endocrinol Metab | year= 2012 | volume= 97 | issue= 11 | pages= E2084-9 | pmid=22904181 | doi=10.1210/jc.2012-2298 | pmc=3485588 | url=https://www.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pubmed&tool=sumsearch.org/cite&retmode=ref&cmd=prlinks&id=22904181 }}</ref>
 
== References ==
== References ==
{{Reflist|2}}
{{Reflist|2}}
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Latest revision as of 15:16, 21 July 2017

Congenital adrenal hyperplasia main page

Overview

Classification

21-hydroxylase deficiency
11β-hydroxylase deficiency
17 alpha-hydroxylase deficiency
3 beta-hydroxysteroid dehydrogenase deficiency
Cytochrome P450-oxidoreductase (POR) deficiency (ORD)
Lipoid congenital adrenal hyperplasia

Differential Diagnosis

Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1] Associate Editor(s)-in-Chief: Mohammed Abdelwahed M.D[2]

Overview

Reconstructive surgery and Surgical adrenalectomy.

Surgery

Reconstructive surgery

reconstructive gynecologic surgery as adolescents or adults, including clitoroplasty and vaginoplasty.[1]

Surgical adrenalectomy

The major benefit is lowering adrenal androgen and progesterone secretion. However, It increases dependency on glucocorticoid and mineralocorticoid replacement therapy.[2]

References

  1. Premawardhana LD, Hughes IA, Read GF, Scanlon MF (1997). "Longer term outcome in females with congenital adrenal hyperplasia (CAH): the Cardiff experience". Clin Endocrinol (Oxf). 46 (3): 327–32. PMID 9156043.
  2. Crocker MK, Barak S, Millo CM, Beall SA, Niyyati M, Chang R; et al. (2012). "Use of PET/CT with cosyntropin stimulation to identify and localize adrenal rest tissue following adrenalectomy in a woman with congenital adrenal hyperplasia". J Clin Endocrinol Metab. 97 (11): E2084–9. doi:10.1210/jc.2012-2298. PMC 3485588. PMID 22904181.