Catecholaminergic polymorphic ventricular tachycardia differential diagnosis

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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]; Associate Editor(s)-in-Chief: Mounika Reddy Vadiyala, M.B.B.S.[2]

Overview

Catecholaminergic polymorphic ventricular tachycardia must be differentiated from Arrhythmogenic right ventricular dysplasia, Short-coupled ventricular tachycardia (SC-torsade de pointes [TdP]), Long QT syndrome and Andersen-Tawil syndrome.

Differentiating Catecholaminergic polymorphic ventricular tachycardia from other Diseases

Catecholaminergic polymorphic ventricular tachycardia must be differentiated from other diseases that cause syncope, ventricular tachycardia, and sudden cardiac death, such as:

Differentiating Catecholaminergic polymorphic ventricular tachycardia from other diseases on the basis of syncope, sudden cardiac death, and ventricular tachycardia

On the basis syncope, sudden cardiac death, and ventricular tachycardia, Catecholaminergic polymorphic ventricular tachycardia must be differentiated from Arrhythmogenic right ventricular dysplasia, Short-coupled ventricular tachycardia (SC-torsade de pointes TdP), Long QT syndrome, Andersen-Tawil syndrome and Brugada syndrome.

Diseases Cause Clinical manifestations ECG Structural abnormalities
Resting ECG ECG during exercise or stress
Arrhythmogenic right ventricular dysplasia
Short-coupled ventricular tachycardia

(SC-torsade de pointes TdP)

Long QT syndrome
Andersen-Tawil syndrome
Brugada syndrome
Differential Diagnosis 6

References

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