Capillary leak syndrome: Difference between revisions
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==Prognosis== | ==Prognosis== |
Revision as of 19:37, 28 January 2013
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Editor-In-Chief: C. Michael Gibson, M.S., M.D. [1]
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Synonyms and Keywords: Systemic capillary leak syndrome; SCLS; Clarkson's disease.
Prognosis
Mortality is reported in 21% of the 57 cases described. However, better management of this condition has recently led to lower mortality.
In the Mayo Clinic’s experience, the median survival of 25 patients that were followed over 30 years (counting only SCLS-related deaths) was approximately 15 years, and their 5-year survival rate was 76%.[1][2] In European experience, the 5-year post-diagnosis survival rate was 85% in 23 patients who had received prophylactic treatment and 20% in 5 patients who had not.[3] However, better identification and management of this condition appears to be resulting in lower mortality and improving survival and quality-of-life results as of late.
Diagnosis
Symptoms
Generalized swelling may be present.
Physical Examination
Vitals
Skin
Laboratory Studies
- Hemoconcentration
- Hypoalbuminemia without albuminuria